Development of Right Ventricular Obstruction by Aberrant Muscular Bands

Publisher Website
Google Scholar
Abstract
The congenital cardiac malformation referred to as the "2 chambered right ventricle" in recent publications is characterized by aberrant hyper-trophied muscular bands which divide the right ventricular cavity into a high pressure chamber located immediately distal to the tricuspid valve annulus and a low pressure chamber distal to the hypertrophied muscle bands. The bands produce an effective obstruction to the flow of blood from the right atrium to the pulmonary artery. Thirteen of the 15 reported cases also had an interventricular septal defect. The malformation should not be confused with tetralogy of Fallot because the obstructive hypertrophic bands are usually proximal to the right ventricular infundibulum. The diagnosis may be suspected at time of cardiac catheterization and firmly established with selective angiocardiography and this malformation is amenable to surgical correction. The purpose of this report is to show that the aberrant muscular bands, although present, may be non-obstructive in early infancy and that the obstructive effect is developed with time as the bands become progressively more hypertrophied. This is based upon a study of 3 patients by catheterization and angiocardiography at intervals of 1-1 /2 to 2 years.

This publication has 2 references indexed in Scilit: