Congenital Soft Tissue Dysplasia: A New Malformation Entity and Concept

Abstract
Until recently, management of pathological conditions of soft tissue was scattered among subspecialities according to the clinical presentation: dermatologists, vascular surgeons, orthopaedists, plastic surgeons, neurologists, neurosurgeons, and, of course, paediatric surgeons all took their turn. The pathological conditions were termed giant hamartomas, segmentary gigantism, hypertrophic limbs, phacomatosis, angiodysplasia; or were grouped in syndromes such as Parkes-Weber or Klippel-Trenaunay. Hardly anything was known about their embryological or physiopathological development, and consequently complete cure was impossible.