Progressive Esophageal Dysfunction in Chronic Granulomatous Disease
- 1 January 1982
- journal article
- case report
- Published by Wiley in Journal of Pediatric Gastroenterology and Nutrition
- Vol. 1 (1) , 145-150
- https://doi.org/10.1097/00005176-198201010-00024
Abstract
Chronic granulomatous disease of childhood (CGD), a hereditary disorder of neutrophil function, affects the gastrointestinal tract in a variety of ways. Esophageal involvement has only rarely been reported. An 11-year-old boy with CGD and progressive esophageal dysmotility is described. Repeated radiographic, endoscopic, and motility studies revealed a markedly atonic esophagus with varying function of the lower esophageal sphincter. Pharmacologic therapy and esophageal dilatations were unsuccessful in establishing adequate esophageal function. A feeding gastrostomy was required for nutritional support.Keywords
This publication has 0 references indexed in Scilit: