Familial primary cutaneous amyloidosis. Clinical, genetic, and immunofluorescent studies
- 1 August 1978
- journal article
- research article
- Published by American Medical Association (AMA) in Archives of Dermatology
- Vol. 114 (8) , 1173-1176
- https://doi.org/10.1001/archderm.114.8.1173
Abstract
Familial primary cutaneous amyloidosis, a rare, autosomal dominant genodermatosis, affected 16 of 46 family members of German descent. Previous case reports involved families of Russian, Spanish or Chinese descent. The finding of Ig[immunoglobulin]G, IgM, C3 [complement component 3] in the amyloid deposits confirms recent reports of immunofluorescent dermal amyloid deposits.This publication has 4 references indexed in Scilit:
- Immunofluorescence studies in primary localized cutaneous amyloidosisBritish Journal of Dermatology, 1977
- Familial Generalized Dyschromic Amyloidosis CutisJournal of Cutaneous Pathology, 1976
- Lichen AmyloidosusJournal of Investigative Dermatology, 1965
- Amyloidosis CutisArchives of Dermatology, 1963