Polysaccharide (Amylopectin-like) Storage Myopathy Histochemical, Ultrastructural and Biochemical Studies
- 1 January 1981
- book chapter
- Published by Springer Nature
- Vol. 7, 292-296
- https://doi.org/10.1007/978-3-642-81553-9_84
Abstract
A case of an adult polysaccharide myopathy is reported in a patient with progressive muscular atrophy and weakness of limb girdles. Histochemistry and electron microscopy showed in some muscle fibers, a storage material composed of amylopectin-like filaments. Biochemical results were normal and no enzyme deficiency was found. This case is compared with three other published cases. Pathological conditons with amylopectin or amylopectin-like storage material are reviewed.Keywords
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