Cardiomyopathy in a Case of Crow-Fukase Syndrome.
- 1 January 1997
- journal article
- case report
- Published by International Heart Journal (Japanese Heart Journal) in Japanese Heart Journal
- Vol. 38 (6) , 877-880
- https://doi.org/10.1536/ihj.38.877
Abstract
Crow-Fukase syndrome or POEMS syndrome is a variant of plasma cell dyscrasia that is characterized by polyneuropathy, organomegaly, endocrinopathy, the presence of M-protein in serum, and dermatological changes. A 60-year-old man presented with features of Crow-Fukase syndrome, such as the presence of M-protein in serum, dermatological changes, and osteosclerotic changes, but did not have polyneuropathy. To our knowledge, this is the first case of Crow-Fukase syndrome in which the presence of hypertrophic cardiomyopathy has been confirmed by a left endomyocardial biopsy. The findings suggest that hypertrophic cardiomyopathy may be a manifestation of organomegaly in patients with Crow-Fukase syndrome.Keywords
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