Recessive ataxia in Acadians and “Cajuns”
- 1 November 1984
- journal article
- research article
- Published by Cambridge University Press (CUP) in Canadian Journal of Neurological Sciences
- Vol. 11 (S4) , 526-533
- https://doi.org/10.1017/s0317167100034995
Abstract
The physician exposed to a large number of patients with a recessive form of ataxia, will occasionally observe slower progression forms which lack many of the severe features or cardinal symptoms of Friedreich's disease. We have studied 31 such cases in Acadians of the Maritime Provinces of Canada, and in their separated from Louisiana, now called . These patients are compared to a consecutive series of 22 Friedreich's disease cases in French Canada.This publication has 7 references indexed in Scilit:
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