Biópsia do nervo sural na distrofia muscular miotônica
Open Access
- 1 March 1996
- journal article
- clinical trial
- Published by FapUNIFESP (SciELO) in Arquivos de Neuro-Psiquiatria
- Vol. 54 (1) , 19-24
- https://doi.org/10.1590/s0004-282x1996000100003
Abstract
Foram estudados 12 pacientes com distrofia muscular miotônica com o objetivo de verificar o comprometimento do sistema nervoso periférico. Todos apresentavam os sinais e sintomas principais da doença. Nenhum tinha outras causas que pudessem justificar uma polineuropatia. Todos foram submetidos a biópsia do nervo sural com contagem de fibras mielínicas e realização de histograma. Dois não apresentavam histograma bimodal. Os pacientes mostraram redução do número de fibras mielínicas. Concluímos que a polineuropatia pode fazer parte do quadro clínico polimorfo da distrofia muscular miotônica.Keywords
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