Transatrial repair of double-outlet right ventricle in infants.

Abstract
In 3 infant cases of double outlet right ventricle (DORV), 2 with normally related great arteries (NGA) and 1 with side-by-side great arteries, a transatrial repair was performed. In all 3 cases, the results were excellent. In the small baby with DORV with NGA and in DORV with side-by-side great arteries with a hypoplastic crista, a transatrial repair should be successful. This is dependent on the VSD [ventricular septal defect] being in the perimembranous (and therefore subaortic) location and on the absence of infundibular pulmonary stenosis. In all other varieties of DORV, the repair should probably be done through the ventricle.