Aicardi's Syndrome With Multiple Papilloma of Choroid Plexus

Abstract
To the Editor.— The association of Aicardi's syndrome with multiple papilloma of the choroid plexus has been described in a 13-month-old female infant and a 4-year-old girl.1We describe another example of this association in a female infant. Report of a Case.— The clinical features of our infant included alternately lateralized clonic convulsions since 4 weeks of age; these convulsions were replaced by asymmetric infantile spasms since 3 months of age, agenesis of the corpus callosum, occipital flattening, numerous pale yellow areas in the ocular fundi, scoliosis, and hemivertebrae. When she was awake, her EEG findings included supression-burst activities in the left hemisphere and hypsarrhythmia in the right hemisphere. When the infant was asleep, a complete asynchrony was observed in the supression-burst activities between the two hemispheres. Computed tomography at the age of 1 month disclosed two protruding masses in the infant, one each in the third and right

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