XANTHOMATOSIS: IV. LIPOID PROTEINOSIS (PHOSPHATIDE LIPOIDOSIS)
- 1 April 1939
- journal article
- research article
- Published by American Medical Association (AMA) in JAMA Otolaryngology–Head & Neck Surgery
- Vol. 29 (4) , 650-661
- https://doi.org/10.1001/archotol.1939.00650050698006
Abstract
There are various types of xanthoma which may result in lesions involving the mucous membranes of the mouth, throat, larynx and trachea. We wish to report a case of lipoid proteinosis (Urbach1) in which such lesions were presented and to demonstrate that this condition is a definite clinical and especially a definite histologic and histochemical entity. It will be differentiated especially from other forms of xanthomatosis involving the mucous membranes, such as disseminate xanthomatosis, hepatosplenomegaly with lipoidosis of the skin and mucous membrane of Bürger and Grütz, and in some cases Hand-Schüller-Christian disease.2 Lipoid proteinosis was first recognized as a form of xanthomatosis by Urbach3and by Urbach and Wiethe in 1929,4under the title "lipoidosis cutis et mucosae," although it had been described by Siebenmann5in 1908 and by Wiethe6in 1924 and in 1926 as a hyaline change of the mucous membranes associated with hyperkeratotic lesions of theKeywords
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