Abstract
One case of embryonal paratesticular sarcoma and 2 cases of leiomyosarcomas are reported. A 13 yr old boy with embryonal sarcoma is well after an orchiectomy and high ligation of the spermatic cord followed by radiotherapy and chemotherapy. A 66 yr old man was doing well after orchiectomy and hemiscrotectomy for a paratesticular leiomyosarcoma. The 3rd patient had a highly pleomorphic leiomyosarcoma and died 2 months postoperatively. The clinical and histological diagnosis of paratesticular rhabdomyosarcomas and leiomyosarcomas is reviewed and the various therapeutic approaches to these neoplasms are discussed. Retroperitoneal lymph node dissection, radiotherapy and chemotherapy are important adjuncts to orchiectomy in the management of rhabdomyosarcomas. Retroperitoneal lymph node dissection and radiotherapy are not indicated in leiomyosarcomas, since these neoplasms tend to metastasize by the hematogenous route and are radioresistant. Chemotherapy has yet to be evaluated in the management of paratesticular leiomyosarcomas.