Pulmonary Function in Myositis Ossificans Progressiva 1
- 1 September 1974
- journal article
- case report
- Published by American Thoracic Society in American Review of Respiratory Disease
- Vol. 110 (3) , 333-337
- https://doi.org/10.1164/arrd.1974.110.3.333
Abstract
Pulmonary function was evaluated in a patient with myositis ossificans progressiva, a rare disorder characterized by ossification of muscles, fascia, tendons, and ligaments, and associated with congenital digital anomalies. Results showed diminished lung volumes with normal airway dynamics and lung elastic recoil, suggesting a restricted chest cage disorder.Keywords
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