α 1 -Antitrypsin Deficiency: A Variant with No Detectable α 1 -Antitrypsin

Abstract
No α 1 -antitrypsin could be detected in the serum of a 24-year-old man with advanced pulmonary emphysema by agarose electrophoresis, immunoelectrophoresis, double diffusion in agarose gel, or α 1 -antitrypsin genetic typing by a combination of starch-gel electrophoresis and crossed antigen-antibody electrophoresis. A circulating α 1 -antitrypsin inactivator could not be demonstrated. Evidence was obtained in family members of genetic transmission of this new α 1 -antitrypsin variant.

This publication has 10 references indexed in Scilit: