Autosomal dominant vitreoretinochoroidopathy (ADVIRC).

Abstract
The 2nd family recognized to have autosomal dominant vitreoretinochoroidopathy is reported. The clinical features were autosomal dominant inheritance; peripheral, coarse pigmentary degeneration of the fundus for 360.degree., with a relatively discrete posterior border in the equatorial region (this finding may be pathognomonic); superficial punctate yellowish-white opacities in the retina; various vascular abnormalities; breakdown of the blood-retinal barrier; retinal neovascularization; vitreous abnormalities; and choroidal atrophy. Visual reduction was mainly due to macular edema or vitreous hemorrhage.

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