Camurati-Engelmann disease (progressive hereditary craniodiaphyseal dysplasia)
- 1 January 1978
- journal article
- research article
- Published by Journal of Neurosurgery Publishing Group (JNSPG) in Journal of Neurosurgery
- Vol. 48 (1) , 138-142
- https://doi.org/10.3171/jns.1978.48.1.0138
Abstract
In a patient with Camurati-Engelmann disease, orbital and optic nerve decompression resulted in improvement of papilledema. Subsequent X-ray films of the optic canals revealed reconstitution of osseous optic canals bilaterally, and papilledema returned in 1 eye. Definitive treatment of this dysplastic metabolic bone disorder rests in the control of rapid abnormal bone formation.This publication has 14 references indexed in Scilit:
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