Glycogen Storage Disease Type I

Publisher Website
Google Scholar
Abstract
To the Editor: The article by Schwenk et al. on enteral glucose administration in children with glycogen storage disease Type I (March 13 issue)1 described the optimal glucose infusion rate required to suppress endogenous glucose production in these patients. Such requirements can be easily satisfied by supplementation of the diet with raw cornstarch, as proposed by Chen et al.2 In that study, all the children except an eight-month-old infant maintained normal blood glucose and lactate levels. The authors suggested that the lack of effect of cornstarch on the infant's blood glucose levels was presumably due to the relatively low level . . .

This publication has 3 references indexed in Scilit: