Abstract
Juvenile dermatitis herpetiformis occurred in a 20 mo. old girl. She had granular Ig[immunoglobulin]A, C3 [complement component 3] and fibrin bound to the basement membrane zone of the skin by direct immunofluorescence and negative serum antibodies against the skin on indirect immunofluorescence. The HLA typing of peripheral lymphocytes was A1, Aw30, B8, Bw51 without clinical evidence of malabsorption syndrome. A rapid improvement was observed on dapsone therapy. Juvenile dermatitis herpetiformis is apparently a disease entity different from chronic bullous dermatosis of childhood.