Abstract
A case is described of congenitally corrected transposition of the great arteries (atrioventricular discordance, ventriculoarterial discordance) with interrupted aortic arch, a previously unreported association. Aortic continuity was achieved by direct surgical anastomosis. Pulmonary artery banding was subsequently necessary, because of heart failure associated with a large ventricular septal defect. A possible pathogenetic mechanism is suggested.