Radiological finding in lipoid proteinosis

Abstract
Lipoid proteinosis (Urbach-Weithe disease or Hyalinosis Cutis et Mucosae) is a rate autosomal recessive disease of unknown etiology involving the skin and mucous membranes of the upper aerodigestive passages. More recently, it has been recognized as a generalized disorder which can also involve the CNS, lung, lymph nodes and striated muscles. The aim of this work is to study the radiographic features of this disease.

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