Phenotypic Alteration of Vascular Smooth Muscle Cells Precedes Elastolysis in a Mouse Model of Marfan Syndrome
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- 19 January 2001
- journal article
- other
- Published by Wolters Kluwer Health in Circulation Research
- Vol. 88 (1) , 37-43
- https://doi.org/10.1161/01.res.88.1.37
Abstract
—Marfan syndrome is associated with early death due to aortic aneurysm. The condition is caused by mutations in the gene (FBN1) encoding fibrillin-1, a major constituent of extracellular mi...Keywords
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