Principles of Management of the Persistent Cloaca in the Female Newborn

Abstract
The persistent cloaca in the female newborn is one of the more complex and challenging developmental malformations that the pediatric urologist encounters. A review of 5 patients and 34 completely documented cases was undertaken to characterize the defects and devise a logical diagnostic and therapeutic approach. Diagnostic steps included the search for associated anomalies, which were present in the upper urinary tract (33%), gastrointestinal tract (13%), cardiovascular system (13%), CNS (10%) and respiratory tract (5%). Delineation of the cloaca and its anatomic relationships was determined by abdominal X-rays, injection of contrast material into the cloacal channel, excretory urography and endoscopy with selective catherterization. Surgical treatment began with a diverting right transverse colostomy in the newborn period followed by rectal pull-through when the patient weighed 25 lb. Vaginal pull-through was performed at the same time as the rectal pull-through when the vagina entered the cloaca high. If the cloacovaginal communication was low, a vaginoplasty by a posterior flap procedure was done when the child was 10-12 yr old. Even if anatomy was reconstructed in an ideal manner urinary and fecal continence could not be assured since congenital neurologic dysfunction was not uncommon.

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