Coronary Arteriomegaly in a Patient with Ehlers-Danlos Syndrome and Multiple Aneurysms
- 1 November 2003
- journal article
- research article
- Published by SAGE Publications in Angiology
- Vol. 54 (6) , 733-736
- https://doi.org/10.1177/000331970305400616
Abstract
The authors report a case of coronary arteriomegaly in a patient with Ehlers-Danlos syndrome and multiple aneurysms who presented with myocardial infarction. Coronary arteriography revealed distal "pruning" of vessels without occlusive disease. Fibroblast cultures excluded Ehlers-Danlos syndrome types IV and VII. Literature review suggests this may represent a previously unidentified vascular syndrome.Keywords
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