INTUSSUSCEPTION IN PATIENTS WITH CYSTIC FIBROSIS

Abstract
Intussusception is one of the lesser known intestinal complications of cystic fibrosis and occurs in approximately 1% of patients. Clinical details are presented of 22 episodes of intussusception occurring in 19 patients over 4 years of age. The average age at onset was 9 9/12 years (Range 4 to 16 years). Most patients were in good or excellent clinical condition and all had pancreatic insufficiency. An operation was performed for 19 of the 22 episodes; resection was required twice. The etiology of the intussusception was felt to be the accumulation of thick putty-like inspissated material in the cecum. Reasons are given for urging the judicious use of the barium enema as a means of reducing the intussusception. Intussusception occurs more frequently than commonly thought and may even be the presenting complaint of the undiagnosed patient with cystic fibrosis.

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