Recessive dystrophic epidermolysis bullosa. Part 2: care of the adult patient

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Abstract
This article is the second in a series of three focusing on the causes, clinical presentation, complications and care of adult patients affected by epidermolysis bullosa (EB) – a group of rare genetic skin fragility disorders. The emphasis of this article will be on the nursing care of adults with recessive dystrophic EB (RDEB). RDEB patients are never ‘wound free’ and the challenge to provide effective wound care is immense. This article details some of the basic practical wound care issues to be considered when caring for a patient with EB, particularly RDEB, emphasizing the need for a holistic approach, with strong patient involvement. Minimizing and preventing trauma, generating an optimal wound healing environment, and the management of pain and pruritis will also be discussed.