Intractable Epidermolysis bullosa acquisita: Efficacy of Ciclosporin A

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Abstract
We report the case of a 66-year-old man who presented with a spontaneous blistering involving both skin and mucous membranes diagnosed as an inflammatory form of epidermolysis bullosa acquisita. During a 5-year course the condition failed to respond to various therapies. Finally, only ciclosporin, together with a low dose regimen of prednisone, achieved a dramatic improvement with a total clearing within 6 months, persisting 1½ years after discontinuation. Such results prompt us to propose such an association as a primary therapeutic scheme in an otherwise barely tractable disease.

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