MEDULLARY CARCINOMA OF THE THYROID WITH ECTOPIC ACTH SYNDROME

Abstract
An autopsied patient with medullary carcinoma of the thyroid and ectopic ACTH syndrome is reported. A microadenoma of pancreatic islet coexisted in this case, which is assumed to be of D cell origin. Immunohistochemical study revealed decreased number of pituitary ACTH cells. Some of them showed Crooke''s degeneration. Hormone assay study of tumor tissue and plasma disclosed abnormal ACTH, .beta.-MSH and calcitonin. Somatostatin and Substance P were also demonstrated in tissue. Histologically the tumor showed solid alveolar pattern with a minor part consisting of small cell variant and this histologic variation is discussed.