Present criteria for the diagnosisin vivoof olivopontocerebellar atrophy

Abstract
We present 6 cases of olivopontocerebellar atrophy (OPCA) of Dèjérine-Thomas type. The diagnosis was based on an appropriate clinical picture, anomalous brainstem auditory evoked potentials (BAEP) and computerized tomography (CT) and/or magnetic nuclear resonance (MNR) imaging which demonstrated atrophy of the cerebellum and the pons. We believe that these methods will provide greater uniformity in the diagnosis of such an heterogeneous entity as OPCA.