Idiopathic Retroperitoneal Fibrosis and Necrotizing Vasculitis: Report of a Case, With Autopsy Findings and Etiologic Consideration

Abstract
ORMOND,1–3 is generally considered to be the first person to recognize the entity of idiopathic retroperitoneal fibrosis. Since his report in 1948 numerous case reports have been published, with remarkably little variation in the clinical and pathologic findings. Kay4 recently reviewed the world literature and summarized the findings in 125 cases. The disease is believed to be increasing in incidence.5