Ebstein's Disease

Abstract
EBSTEIN'S disease,1 a rare congenital anomaly that accounts for less than 1 per cent of all congenital heart disease, is characterized by malformation and downward displacement of the tricuspid valve. The cusps are grossly malformed and present a curious basketlike arrangement. Although the anterior cusp retains some attachment to the atrioventricular ring, the rest of the valve is attached lower down to the walls of the right ventricle.2 The anatomic right ventricle is thus divided into two chambers: one proximal to the valve, which is grossly dilated and thin walled and continuous with the right atrium; and a distal chamber . . .

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