Phytanic acid α-oxidation: identification of 2-hydroxyphytanoyl-CoA lyase in rat liver and its localisation in peroxisomes
- 22 September 1999
- journal article
- Published by Elsevier in Biochimica et Biophysica Acta (BBA) - Molecular and Cell Biology of Lipids
- Vol. 1440 (2-3) , 176-182
- https://doi.org/10.1016/s1388-1981(99)00126-2
Abstract
No abstract availableKeywords
This publication has 33 references indexed in Scilit:
- Refsum disease is caused by mutations in the phytanoyl–CoA hydroxylase geneNature Genetics, 1997
- Identification of PAHX, a Refsum disease geneNature Genetics, 1997
- Phytanoyl-CoA Hydroxylase Is Present in Human Liver, Located in Peroxisomes, and Deficient in Zellweger Syndrome: Direct, Unequivocal Evidence for the New, Revised Pathway of Phytanic Acid α-Oxidation in HumansBiochemical and Biophysical Research Communications, 1996
- Phytanic acid must be activated to phytanoyl-CoA prior to its α-oxidation in rat liver peroxisomesBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1994
- Studies on phytanic acid α-oxidation in rat liver and cultured human skin fibroblastsBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1993
- Characteristics and subcellular localization of pristanoyl-CoA synthetase in rat liverBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1992
- Identification of pristanoyl-CoA oxidase as a distinct, clofibrate non-inducible enzyme in rat liver peroxisomesBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1992
- Mitochondrial oxidation of phytanic acid in human and monkey liver: Implication that Refsum's disease is not a peroxisomal disorderBiochemical and Biophysical Research Communications, 1990
- The subcellular localization of phytanic acid oxidase in rat liverBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1987
- Activity of peroxisomal enzymes and intracellular distribution of catalase in Zellweger syndromeBiochemical and Biophysical Research Communications, 1984