Homozygosity for the W151X stop mutation in the ?7-sterol reductase gene (DHCR7) causing a lethal form of Smith-Lemli-Opitz syndrome: Retrospective molecular diagnosis
- 13 November 2000
- journal article
- case report
- Published by Wiley in American Journal of Medical Genetics
- Vol. 95 (2) , 174-177
- https://doi.org/10.1002/1096-8628(20001113)95:2<174::aid-ajmg16>3.0.co;2-9
Abstract
No abstract availableKeywords
This publication has 20 references indexed in Scilit:
- Incidence of Smith-Lemli-Opitz syndrome in SlovakiaAmerican Journal of Medical Genetics, 2000
- Smith-Lemli-Opitz syndrome: evidence of T93M as a common mutation of Δ7-sterol reductase in Italy and report of three novel mutationsEuropean Journal of Human Genetics, 1999
- Molecular genetics of the Smith-Lemli-Opitz syndrome and postsqualene sterol metabolismCurrent Opinion in Lipidology, 1999
- Further delineation of the classical Smith-Lemli-Opitz syndrome phenotype at different patient agesClinical Dysmorphology, 1999
- Mutations in the Δ7-sterol reductase gene in patients with the Smith–Lemli–Opitz syndromeProceedings of the National Academy of Sciences, 1998
- Cholesterol metabolism and embryogenesisTrends in Genetics, 1998
- Molecular cloning and expression of the human Δ7-sterol reductaseProceedings of the National Academy of Sciences, 1998
- Clinical and biochemical spectrum of patients with RSH/Smith-Lemli-Opitz syndrome and abnormal cholesterol metabolismAmerican Journal of Medical Genetics, 1997
- Holoprosencephaly in RSH/Smith-Lemli-Opitz syndrome: Does abnormal cholesterol metabolism affect the function ofsonic hedgehog?American Journal of Medical Genetics, 1996
- Defective cholesterol biosynthesis in Smith-Lemli-Opitz syndromeThe Lancet, 1993