The Ocular Pathology of Marfan's Syndrome

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Abstract
Because of numerous and striking ocular abnormalities, Marfan's syndrome has always interested ophthalmologists. In spite of the clinical interest and the shortened life span of many of these patients, few histopathologic studies of the Marfan eye have been reported. Theobald,1in 1941, presented the first histologic report, and Reeh and Lehman,2in 1954, the second. Other less detailed studies were reported by Fischl,3Bergstrand,4Moses,5and Tobin.6Recently, Burian and Allen7described in detail the histopathology of the chamber angle of the previously reported cases of Theobald, Reeh and Lehman, and de Buen and Velazquez. They demonstrated unusual abnormalities of the chamber angle indicating an atavistic anomaly. These included prominent pectinate ligament fibers, anomalies of the outflow channel system, underdevelopment of the circular ciliary muscle, disarrangement of uveal trabecular fibers connecting with the ciliary muscles, and passage of longitudinal muscle fibers internal to

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