Anaesthetic problems in Hurler‐Scheie syndrome. Report of two cases
- 1 August 1986
- journal article
- research article
- Published by Wiley in Acta Anaesthesiologica Scandinavica
- Vol. 30 (6) , 484-486
- https://doi.org/10.1111/j.1399-6576.1986.tb02459.x
Abstract
Hurler‐Scheie syndrome is an intermediate form of mucopolysaccharidosis. Affected patients characterstically present in infancy with serious abnormalities including the upper airways and the lungs. We present two patients with Hurler‐Scheie syndrome and describe their anaesthetic management. One caw was complicated by difficult endotracheal intubation and postoperative pneumonia. The second casr was successfully miinagtd using spinal anaesthesia and mild sedation.Keywords
This publication has 11 references indexed in Scilit:
- Two-stage Fiberoptic Nasotracheal Intubation in InfantsAnesthesiology, 1985
- Anaesthetic considerations in the mucopolysaccharidosesAnaesthesia, 1984
- Anaesthetic Implications of the Mucopolysaccharidoses: A Fifteen-Year Experience in a Children's HospitalAnaesthesia and Intensive Care, 1983
- Airway Management for a Neonate with Congenital Fusion of the JawsAnesthesiology, 1979
- Fiberoptic Bronchoscopic Nasotracheal Intubation in ChildrenChest, 1979
- Spastic quadriparesis due to C1–C2 subluxation in hurler syndromeThe Journal of Pediatrics, 1978
- Anaesthesia in a patient with an unstable neck.Anaesthesia, 1975
- Two cases of Hunter's syndrome—The anaesthetic and operative difficulties in oral surgeryBritish Journal of Oral Surgery, 1972
- Heritable disorders of connective tissue: Surgical and anesthetic problemsJournal of Pediatric Surgery, 1967