The Problem of Unrecognized "Mild Hemophilia"

Abstract
THE WORD "HEMOPHILIA" frequently conjures up the picture of a severely disabled boy or adult man, crippled by damage to his joints, and suffering from recurrent life-threatening hemorrhages. Such patients have the disease in its severe form, usually having less than 1% of normal antihemophilic factor (AHF) (factor VIII) plasma thromboplastin component or (PTC) (factor IX). Less well known is the fact that hemophiliacs with a mild form of the disease may be entirely unaware of their disability. These patients usually have more than 5% of the deficient factor, rarely have trouble with their joints, and are often able to lead a full and normal life. They are nevertheless susceptible to severe bleeding, particularly after surgery or major injury; sometimes ignorance of their inherent bleeding tendency can lead to results more serious than those in a known severe hemophiliac with the same type of bleeding because of delay in instituting

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