Phase I Trial of Pirfenidone in Children with Neurofibromatosis 1 and Plexiform Neurofibromas

This publication has 13 references indexed in Scilit:

• Desmoid tumors in familial adenomatous polyposis: a pilot project evaluating efficacy of treatment with pirfenidone
  American Journal of Gastroenterology, 2003
• Open-label Compassionate Use One Year-treatment with Pirfenidone to Patients with Chronic Pulmonary Fibrosis.
  Internal Medicine, 2002
• Mortality in Neurofibromatosis 1: An Analysis Using U.S. Death Certificates
  American Journal of Human Genetics, 2001
• Malignancy in Neurofibromatosis Type 1
  The Oncologist, 2000
• Survival of Human Neurofibroma in Immunodeficient Mice and Initial Results of Therapy With Pirfenidone
  BioMed Research International, 2000
• Plexiform neurofibromas
  American Journal of Medical Genetics, 1999
• Prognostic signs in the surgical management of plexiform neurofibroma: The Children’s Hospital of Philadelphia experience, 1974-1994
  Published by Elsevier ,1997
• The Growth Regulation of Neurofibroma Cells in Neurofibromatosis Type-1: Increased Responses to PDGF-BB and TGF-β1
  Biochemical and Biophysical Research Communications, 1994
• Growth and Collagen Synthesis of Cultured Neurofibroma Fibroblasts
  The Journal of Dermatology, 1992
• VON RECKLINGHAUSEN NEUROFIBROMATOSIS
  Brain, 1988