The First Cases of Fitzgerald Factor Deficiency in the Orient: Three Cases in One Family
- 1 January 1980
- journal article
- research article
- Published by S. Karger AG in Acta Haematologica
- Vol. 63 (2) , 107-113
- https://doi.org/10.1159/000207379
Abstract
Asymptomatic, female, 56 yr old identical Japanese twins had a severe abnormality in the surface-mediated intrinsic coagulation, fibrinolysis and esterolytic activity. These defects were probably due to the lack of Fitzgerald factor, because of the prolongations of kaolin-activated partial thromboplastin time and kaolin-activated euglobulin lysis time that were not corrected by the addition of Fitzgerald trait-plasma but were corrected to normal levels by the addition of isolated bovine high MW kininogen, Fletcher trait-plasma or Hageman trait-plasma.Keywords
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