Consensus criteria for the diagnosis of frontotemporal cognitive and behavioural syndromes in amyotrophic lateral sclerosis
Top Cited Papers
- 1 January 2009
- journal article
- Published by Taylor & Francis in Amyotrophic Lateral Sclerosis
- Vol. 10 (3) , 131-146
- https://doi.org/10.1080/17482960802654364
Abstract
Amyotrophic lateral sclerosis (ALS) is increasingly recognized to be a multisystem disorder which includes both clinical and neuropathological features of a frontotemporal lobar degeneration (FTLD). In order to provide a common framework within which to discuss the characteristics of the cognitive and behavioural syndromes of ALS, and with which to conduct clinical and neuropathological research, an international research workshop on frontotemporal dementia (FTD) and ALS was held in London, Canada in June 2007. The recommendations arising from this research workshop address the requirement for a concise clinical diagnosis of the underlying motor neuron disease (Axis I), defining the cognitive and behavioural dysfunction (Axis II), describing additional non-motor manifestations (Axis III) and identifying the presence of disease modifiers (Axis IV).Keywords
This publication has 109 references indexed in Scilit:
- Identification of new ANG gene mutations in a large cohort of Italian patients with amyotrophic lateral sclerosisneurogenetics, 2007
- Progranulin mutations and amyotrophic lateral sclerosis or amyotrophic lateral sclerosis-frontotemporal dementia phenotypesJournal of Neurology, Neurosurgery & Psychiatry, 2006
- TDP-43 is a component of ubiquitin-positive tau-negative inclusions in frontotemporal lobar degeneration and amyotrophic lateral sclerosisBiochemical and Biophysical Research Communications, 2006
- The Addenbrooke's Cognitive Examination Revised (ACE‐R): a brief cognitive test battery for dementia screeningInternational Journal of Geriatric Psychiatry, 2006
- National Institute of Neurological Disorders and Stroke–Canadian Stroke Network Vascular Cognitive Impairment Harmonization StandardsStroke, 2006
- Short NART, CCRT and Spot-the-Word: Comparisons in older and demented personsBritish Journal of Clinical Psychology, 1997
- Frontal Behavioral Syndromes in Cortical and Subcortical DementiaAssessment, 1996
- Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosisNature, 1993
- Normative data stratified by age and sex for 12 neuropsychological testsJournal of Clinical Psychology, 1986
- The Hospital Anxiety and Depression ScaleActa Psychiatrica Scandinavica, 1983