Congenital Pericardial Defect

Abstract
THE FIRST DESCRIPTION of congenital absence of the pericardium was given in 1559 by Realdo Columbus. Since then, over 110 cases have been reported. This relatively rare condition has been diagnosed with increased frequency in the last two decades. The defect is usually partial, involving the entire left portion of the pericardium. Much less common is the defect on the right, or the absence of the entire pericardium.1 Occasionally the defect involves but a small portion of one side, again, usually the left side. In this case the defect gives rise to fairly distinctive signs and symptoms which will not be reviewed here.2-5 Two cases of congenital absence of the pericardium are described in this report, one with complete, the other with left-sided absence of the pericardium. They illustrate the mode of presentation, symptomatology, and method of diagnosis common to many such cases. Report of Cases Case 1

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