Three cases of vascular neurofibromatosis were studied angiographically. Renal artery involvement was present in all. In 1 patient multiple vascular lesions including thoracic outlet arteries, thoracic aorta, pulmonary artery, celiac, superior mesenteric and iliac arteries were also present. Angiography revealed in the involved arteries a smoothly bordered stenotic segment continuing into an elongated funnel-shaped channel. The presence of similar features in another 12 cases reported in the literature implies that the described pattern may be considered as suggestive of vascular neurofibromatosis.