A HISTOLOGICAL AND CHEMICAL STUDY OF THREE CASES OF DIFFUSE CEREBRAL SCLEROSIS
- 1 February 1954
- journal article
- research article
- Published by BMJ in Journal of Neurology, Neurosurgery & Psychiatry
- Vol. 17 (1) , 33-49
- https://doi.org/10.1136/jnnp.17.1.33
Abstract
In the "spongy type" (Canavan) of diffuse cerebral sclerosis, chemical findings suggested an arrest of myelinization of cerebral white matter during late fetal life. In the Pelizaeus-Merzbacher type, probable arrest of myelinization in early childhood with recent cortical degeneration was indicated. In a Krabbe-type case "globoid bodies" contained cerebroside which had excited a microglial reaction.Keywords
This publication has 17 references indexed in Scilit:
- THE CEREBRAL LIPIDS IN DISSEMINATED SCLEROSIS AND IN AMAUROTIC FAMILY IDIOCYBrain, 1953
- LATE INFANTILE METACHROMATIC LEUCO-ENCEPHALOPATHY, WITH PRIMARY DEGENERATION OF THE INTERFASCICULAR OLIGODENDROGLIABrain, 1950
- PATHOLOGY OF DEMYELINATING DISEASES AS AN ALLERGIC REACTION OF THE BRAINArchives of Neurology & Psychiatry, 1944
- Über die Verteilung der Neuraminsäure im Gehirn (Mit einer Mikromethode zur quantitativen Bestimmung der Substanz im Nervengewebe)Hoppe-Seyler´s Zeitschrift Für Physiologische Chemie, 1941
- DIFFUSE SCLEROSIS WITH PRESERVED MYELIN ISLANDSArchives of Neurology & Psychiatry, 1933
- THE ENCEPHALITIS PERIAXIALIS OF SCHILDER. A CLINICAL AND PATHOLOGICAL STUDY, WITH AN ACCOUNT OF TWO CASES, ONE OF WHICH WAS DIAGNOSED DURING LIFEBrain, 1924
- Über einen Fall von herdförmig disseminierter Sklerose des Gehirns bei einem Säugling unter besonderer Berücksichtigung eigenartiger RiesenzellenbefundeVirchows Archiv, 1924
- Zur histopathologie der multiplen sklerose im kindesalterZeitschrift für die gesamte Neurologie und Psychiatrie, 1922
- A NEW FAMILIAL, INFANTILE FORM OF DIFFUSE BRAIN-SCLEROSISBrain, 1916
- Ueber eine eigenthümliche Form spastischer Lähmung mit Cerebralerscheinungen auf hereditärer Grundlage. (Multiple Sklerose)Archiv Fur Psychiatrie Und Nervenkrankheiten, 1885