Disseminated intravascular coagulation complicating systemic juvenile chronic arthritis (”Still's disease”)

Abstract
Two children suffering from systemic juvenile chronic arthritis (JCA)11 complicated by acute disseminated intravascular coagulation (DIG) are described. One had a fatal outcome with acute renal failure and cerebral haemorrhage; the other recovered. Early recognition and treatment of the underlying cause — usually an infection — as well as replacement of clotting factors are important in management.