Adult Polycystic Renal Disease Presenting in Infancy: A Report Emphasizing the Bilateral Involvement
- 1 December 1982
- journal article
- case report
- Published by Wolters Kluwer Health in Journal of Urology
- Vol. 128 (6) , 1290-1291
- https://doi.org/10.1016/s0022-5347(17)53467-9
Abstract
We describe a girl with adult polycystic renal disease that presented as a unilateral abdominal mass on an excretory urogram. The child had a 4-generation family history of this disorder. Clinical course had been unremarkable until she was 12 years old and died of a ruptured intracranial aneurysm. Despite the clinical impression of unilateral renal involvement, postmortem examination showed that the clinically normal kidney had developed early cyst formation in several areas, thus, underscoring the bilateral nature of adult polycystic disease.Keywords
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