Idiopathic Familial Atrial Cardiomyopathy with Diffuse Conduction Block
- 1 April 1989
- journal article
- Published by Oxford University Press (OUP) in QJM: An International Journal of Medicine
- Vol. 71 (1) , 325-332
- https://doi.org/10.1093/oxfordjournals.qjmed.a068328
Abstract
SUMMARY Isolated atrial cardiomyopathy is rare and familial idiopathic atrial cardiomyopathy has only been described once. We describe a case characterized by severely reduced atrial contractile function, intermittent atrial electrical standstill, diffuse interatrial, intraventricular and atrioventricular block, complicated by systemic embolism. Whilst this condition is undoubtedly rare, other cases may be being mistaken for simple sinoarrial disease.Keywords
This publication has 0 references indexed in Scilit: