ORIGIN OF BOTH GREAT VESSELS FROM THE ARTERIAL VENTRICLE: A COMPLEX WITH VENTRICULAR INVERSION

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Abstract
Pathological and clinical features are presented in 3 children with the rare developmental anomaly, origin of both great vessels from the inverted arterial ventricle. In 2 instances, this ventricle was left-sided, while in the case with mirror-image dextrocardia, it was on the right. In each case the pathological features were similar to corrected transposition except that both great vessels took origin from the inverted arterial ventricle. Except for the angio-cardiographic features, the clinical findings were of little value in establishing a definitive diagnosis. Selective angiocardiography from the arterial ventricle is the procedure of choice in establishing the diagnosis. The cardiac anomaly described may also be suspected when cyanotic congenital cardiac disease is associated with congenital absence of the spleen, a syndrome found in each of the 3 cases presented.