UIP, DIP, and All That

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Abstract
It all began with Hamman and Rich. Over a period of four years they encountered four patients with an acute respiratory illness of unknown cause that neither they nor their colleagues at Johns Hopkins Hospital had ever seen before. The disorder was short-lived, generally running its course in weeks to months, but in one patient ending fatally in three days. Dyspnea and cyanosis were striking. At autopsy, they found a "peculiar, progressive, diffuse fibrosis of the pulmonary alveolar walls, leading to deficient aeration of the blood with resulting dyspnea and cyanosis, and to enlargement and eventual failure of the right . . .