Hepatic Cutaneous Porphyria
- 1 April 1964
- journal article
- research article
- Published by American Medical Association (AMA) in Archives of Dermatology
- Vol. 89 (4) , 505-514
- https://doi.org/10.1001/archderm.1964.01590280005001
Abstract
There is reason to suspect that an aberration in purine metabolism may represent part of the defect of the hepatic porphyrias. A case of hepatic cutaneous porphyria of the symptomatic type is reported. The patient was treated with adenosine-5-monophosphate for more than one year. A reduction in urine uroporphyrin excretion, as well as a decreased incidence and severity of photosensitivity reactions were noted.Keywords
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