Visual acuity and visual field impairment in Usher syndrome.

Open Access
Publisher Website
Google Scholar
Abstract
WE previously reported on heterogeneity of vestibular responses, level of hearing deficit, and, to a lesser extent, visual impairment in patients with type 1 and type 2 Usher syndrome (retinitis pigmentosa and congenital hearing loss).1 On the basis of their vestibular responses and level of hearing loss, cases were classified into type 1 or type 2 Usher syndrome. Type 1 patients have severe hearing loss (with a pure-tone average of 100 dB or greater), absent vestibular responses on caloric testing, and unintelligible speech, while type 2 patients have vestibular responses to caloric testing and less severely impaired hearing (pure-tone average most often between 40 and 90 dB), with intelligible speech.

This publication has 2 references indexed in Scilit: