MULTIPLE ADENOMAS AND HEPATOCELLULAR CARCINOMA IN A RENAL TRANSPLANT PATIENT WITH GLYCOGEN STORAGE DISEASE TYPE 1A (VON GIERKE DISEASE)
- 1 July 2001
- journal article
- case report
- Published by Wolters Kluwer Health in Transplantation
- Vol. 72 (2) , 343-344
- https://doi.org/10.1097/00007890-200107270-00033
Abstract
We report on a 42-year-old female patient with glycogen storage disease type 1a (von Gierke disease, GSD 1a) who developed hepatic adenomas and finally a hepatocellular carcinoma 10 years after renal transplantation. The tumor was resected; however, the patient died 6 months later as a result of fulminant carcinoma recurrence. In patients who have GSD 1a with terminal renal failure, combined liver and kidney transplantation may be considered at an early stage of the disease.Keywords
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