Mitochondrial electron transport chain complex dysfunction in a transgenic mouse model for amyotrophic lateral sclerosis
Open Access
- 17 October 2002
- journal article
- research article
- Published by Wiley in Journal of Neurochemistry
- Vol. 83 (3) , 535-545
- https://doi.org/10.1046/j.1471-4159.2002.01112.x
Abstract
Amyotrophic lateral sclerosis is a fatal neurodegenerative disease that causes degeneration of motoneurons. Mutation of Cu,Zn superoxide dismutase (SOD1) is one cause for this disease. In mice, expre...Keywords
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